本文报告了5例颅内脊索瘤,术前CT扫描均提示为一类圆形混杂密度肿物,可有不同程度增强,其中3例位于鞍区,术前诊断为颅咽管瘤,2例位于大脑半球实质内,术前诊断为胶质瘤,术后病理检验证实为脊索瘤。文中对颅内脊索瘤的诊断和治疗进行了讨论,认为大脑半球内脊索瘤虽极罕见,但在进行半球肿瘤的鉴别诊断时亦应考虑此瘤。 This article reports 5 cases of intracranial chordoma, preoperative CT scan prompted a class of circular mixed density tumor, may have varying degrees of enhancement, of which 3 were located in the saddle area, preoperative diagnosis of craniopharyngioma, 2 cases Is located in the essence of the cerebral hemispheres, preoperative diagnosis of gliomas, postoperative pathology confirmed as chordoma. This article discusses the diagnosis and treatment of intracranial chordoma, which is considered as rare in the hemisphere, but should be considered in the differential diagnosis of hemisphere tumors.