先天性狭鼻症是新生儿骨性固有鼻腔显著狭窄,生后引起鼻阻、呼吸困难、哺乳障碍的一种疾患。对10例患儿的临床特征进行报道。男7例,女3例,年龄出生1天～4个月,平均50天。9例生后出现鼻阻、发绀、呼吸困难、哺乳困难。仅1例于生后4个月出现哺乳中发绀。初诊时两侧鼻腔无炎症或轻度炎症,固有鼻腔狭窄。正常新生儿鼻腔外径3.2mm的纤维内窥镜容易通 Congenital narrow nose is nasal neonatal significant stenosis of the nasal cavity, nasal obstruction caused by respiratory failure, dyspnea, a disorder of breastfeeding. The clinical features of 10 children were reported. 7 males and 3 females, aged 1 to 4 months, an average of 50 days. Nine cases of nasal obstruction after birth, cyanosis, difficulty breathing, breastfeeding. Only 1 case appeared cyanosis in lactation 4 months after birth. Neonatal nasal inflammation or mild inflammation on both sides of the newly diagnosed, inherent nasal stenosis. Normal neonatal nasal 3.2mm diameter fiber endoscope easy to pass