Ebstein氏畸形的特征是三尖瓣隔叶和后叶的下移,常呈畸形、有孔或者部份或完全缺如.患者可有心悸、心动过速,在作导管检查时常有发生心律失常的倾向.猝死虽然不多,但是死亡的重要原因.本文旨在评价22例有心动过速反复发作的Ebstein氏畸形患者的临床表现、心动过速机制和内外科治疗.病例概况:22例Ebstein氏畸形患者,男12例,女10例,平均年龄24岁(10～45岁).20例入 Ebstein’s deformity is characterized by the downward movement of the tricuspid valve and posterior leaflet, often deformity, perforated or partial or complete lack of patients may have heart palpitations, tachycardia, catheter catheterization often arrhythmia Of the sudden death though not much, but an important cause of death.This paper aims to evaluate the clinical manifestations, tachycardia and surgical treatment of 22 patients with recurrent tachycardia Ebstein’s disease.Patients: 22 cases of Ebstein Deformity patients, 12 males and 10 females, mean age 24 years (10 to 45 years) .20 cases into