Wegener 肉芽肿是少见疾病,预后凶险,国内自1964首次报告以来,迄今见诸文献报告的仅14例,我院近10余年来曾收治5例,本文将该5例连同国内14例参照国外文献作一对照分析和综合复习,以供参考。命名与分类Klinger 在1931年首次报告2例破坏性副鼻窦炎、肾炎及播散性血管炎患者,并称之为“结节性动脉周围炎边缘病例”,1939年Wegener 先后报告了3例破坏性肉芽肿性鼻炎 Wegener’s granulomatosis is a rare disease with a dangerous prognosis. Since the first report in 1964, only 14 cases have been reported in our country and 5 cases have been treated in our hospital for more than 10 years. In this paper, 5 cases with reference to foreign literature For a comparative analysis and comprehensive review, for reference. Naming and Classification Klinger first reported 2 cases of devastating paranasal sinusitis, nephritis and disseminated vasculitis in 1931 and called them “borderline cases of nodular periarteritis”. In 1939, Wegener reported 3 cases of damage Granulomatous rhinitis