心肌病的临床病理学征象:原发性心肌病并不具有特异性的临床病理特征,其基本临床表现主要取决于受累心肌的范围和部位。临床上诊断本病时必须满足以下六项病理学考虑:(1)心肌壁外的(或主干的)冠状动脉无明显病变;(2)无心脏瓣膜疾病;(3)无体循环或肺循环原发性高血压的表现;(4)无心血管先天性畸形或血液分流存在;(5)无肺实质病变;(6)能明确除外由感染性、代谢性、家族遗传性神经肌肉病、过敏性、中毒性及系统性疾病所致的心肌疾病。就定义而言,心肌是本病的主要受累部位,然而,心包及心内膜亦可呈现有意义的变化,后两者可明显地影响本病的临床表现和病程经过。本病通常具有下列病变特点:(1)一 Cardiomyopathy clinical pathology signs: Primary cardiomyopathy does not have specific clinical and pathological features, the basic clinical manifestations depend mainly on the extent and location of affected myocardium. The clinical diagnosis of this disease must meet the following six pathological considerations: (1) myocardial (or trunk) of the coronary artery without obvious lesions; (2) no valvular heart disease; (3) of the systemic circulation or primary pulmonary circulation (4) no cardiovascular congenital malformations or blood shunts exist; (5) no pulmonary parenchymal lesions; (6) can be clearly excluded by the infectivity, metabolic, familial hereditary neuromuscular disease, allergic, Toxicity and systemic diseases caused by heart disease. In terms of definition, myocardium is the main site involved in the disease. However, the pericardium and endocardium may also present meaningful changes. The latter two may significantly affect the clinical manifestation and course of the disease. The disease usually has the following lesions: (1) one