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β－地中海贫血是一种遗传性慢性溶血性疾病。我们收集了13年以来16例小儿β－地中海贫血，占儿科同期浴血性贫血住院病人25％，占儿科同期住院病人总数1．23％。，其中男孩14例，女孩2例；汉族9例，畲族7例；山区10例，沿海地区6例；－1岁发病14例，－4岁发病1例，－7岁发病1例；临床表现通常为：面色苍白、肝脾肿大、发热、黄疸、淋巴结肿大、排茶色尿。贫血、异形红细胞是实验室检查常见的表现。其他有：血红蛋白抗碱试验、血红蛋白电泳试验均异常，HbA2升高、红细胞酸洗脱试验异常、红细胞脆性试验降低，骨穿检查显示：增生性溶血性贫血。本文讨论了β－地中海贫血的诊断与治疗进展。
β-thalassemia is a hereditary chronic hemolytic disease. We collected 16 cases of β-thalassemia in children since 13 years, accounting for 25% of hospitalized pediatric patients with bloody anemia in the same period, accounting for 1.23% of the total pediatric patients in hospital. , Of which 14 were boys and 2 were girls; 9 were Han and 7 were Shezu; 10 were mountainous and 6 were coastal; 14 were -1-year-old, 1 was -4 years old and 1 was -7 years old. The clinical manifestations Usually: pale, hepatosplenomegaly, fever, jaundice, lymphadenopathy, row of brown urine. Anemia, abnormal red blood cells is a common laboratory test performance. Others are: anti-alkali hemoglobin test, abnormal hemoglobin electrophoresis test, HbA2 increased, erythrocyte acid elution test abnormalities, reduced red blood cell fragility test, bone wear examination showed: hyperplastic hemolytic anemia. This article discusses the diagnosis and treatment of β-thalassemia.