线粒体性脑肌病为一组氧化代谢缺陷的神经肌肉疾病。一般CT 所见有:大脑、小脑萎缩,半球低密度区,基底节钙化。尸检证实低密度区为脑梗塞、软化、胶质增生、海绵样变或局限性水肿。作者报导一例临床症状与CT 呈相对应波动变化的病人。例1 男,29岁,儿童期每年夏日畏光,易疲乏。1982年3月15日出现强直性癫痫和短暂意识障碍。7月23日突发右腿无力,继之有该区Jackson 氏癫痫,CT 见左顶叶有低密度区,脑脊液常规及脑血管造影未见异常。8月发展为右侧运动性癫痫,后 Mitochondrial encephalomyopathy is a group of neuromuscular diseases with oxidative metabolism defects. CT see generally have: the brain, cerebellar atrophy, hemispheric low-density area, basal ganglia calcification. Autopsy confirmed low-density areas of cerebral infarction, softening, glia, sponge-like changes or localized edema. The authors report a case of clinical symptoms and CT showed a corresponding fluctuations in patients. Example 1 male, 29 years old, childhood photophobia summer, easy to fatigue. March 15, 1982 tonic epilepsy and transient disturbance of consciousness. July 23 sudden right leg weakness, followed by the district of Jackson’s epilepsy, CT see the left parietal lobe has a low density, cerebrospinal fluid routine and cerebral angiography showed no abnormalities. August development of the right motor epilepsy, after