先天性孤立肾少见,我科曾遇见4例,均伴有多发畸形,报告如下。 临床资料4例均为男性,年龄2～12岁,左侧2例,右侧2例。就诊原因:面色苍白2例,血尿和多饮、多尿各1例。伴有其它畸形和并发症如下:例1:孵裂、角膜白斑、肾性尿崩症。例2:隐性脊柱裂、先天性心脏病、慢性肾功能不全、肾积水、肺结核。例 Congenital isolated kidney rare, my department had met 4 cases, are associated with multiple deformities, the report is as follows. Four cases of clinical data were male, aged 2 to 12 years old, 2 cases left and 2 cases right. Reasons for treatment: pale in 2 cases, hematuria and polyhydration, polyuria in 1 case. Accompanied by other deformities and complications are as follows: Example 1: Incubation, leukoplakia, nephrogenic diabetes insipidus. Example 2: Recessive spina bifida, congenital heart disease, chronic renal insufficiency, hydronephrosis, tuberculosis. example