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本文报道一例女性Ｆａｂｒｙ氏病的肾脏超微结构表现。该病人除了持续性蛋白尿外，无其它临床症状。电镜下见肾小球脏层上皮细胞胞质内充满嗜锇性、同心圆状的髓鞘样小体，其致密层呈现明暗带相间的结构。本文对电镜在Ｆａｂｒｙ氏病诊断中的作用进行了讨论。
This article reports the renal ultrastructure of a female Fabry’s disease. This patient has no other clinical symptoms except for persistent proteinuria. Under the electron microscope, the cytoplasm of glomerulus parietal epithelial cells was filled with osmium-osmotic and concentric myelin-like bodies, and the dense layer showed the structure of light and dark phase. This article discusses the role of electron microscopy in the diagnosis of Fabry’s disease.