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本文分析了我院1978年11月～1997年1月儿科住院和溶血性疾病1897例1902人次，占同期儿科住院总人次37004的5．14％。1897例中，诊断明确的有1614例（85．08％）。其中最常见为红细胞G—6—PD缺陷症，占40．48％；血红蛋白病、新生儿ABO溶血病分别各占19．35％和16．55％。遗传性球形细胞增多症占1．06％，其它病因未明的溶血性贫血占11．65％。本组病例中，MN血型不合性溶血病及重型p地贫合并Rh血型不合、输血后溶血、重型p地贫合并自身免疫性溶血性贫血各1例。溶血性疾病发病以新生儿期为最高，占半数以上。加强对新生儿高胆溶血的研究尤其是对红细胞G——6——PD缺陷溶血发生的防治，有现实意义。
This article analyzes 1897 cases of pediatric inpatient and hemolytic diseases from November 1978 to January 1997 in 19097, accounting for 5.14% of the total pediatric inpatient 37004 in the same period. In 1897 cases, 1614 cases (85.08%) were well diagnosed. The most common one was G-6-PD deficiency, accounting for 40.48%. Hemoglobinopathies and neonatal ABO hemolytic disease accounted for 19.35% and 16.55% respectively. Hereditary spherocytosis accounted for 1.06%, other causes of unknown hemolytic anemia accounted for 11.65%. This group of patients, MN blood group hemolytic disease and severe p-poor with Rh blood group incompatibility after transfusion hemolysis, severe p-thalassemia with autoimmune hemolytic anemia in 1 case. Hemolytic disease incidence in the neonatal period for the highest, accounting for more than half. To strengthen the study of neonatal hypercholesteremia and hemolysis, especially for the prevention and treatment of erythrocyte G - 6 - PD deficiency hemolysis, is of practical significance.