内胚窦瘤为一种恶性程度较高的生殖细胞来源性腺肿瘤,发生在发育不全的性腺中较少见。现结合本院1例进行讨论。张××,33岁,因原发闭经,下腹部隐痛1周,盆腔肿块入院。患者因原发闭经(23岁时)在外院经盆腔气腹造影诊断为子宫卵巢发育不全。染色体检查为45,×/46,××。诊断为Turner氏综合征,曾 Endodermal sinus tumor is a malignant germ cell-derived adenocarcinoma that occurs less frequently in under-developed gonads. Now with the hospital in 1 case to discuss. Zhang × ×, 33 years old, due to primary amenorrhea, lower abdominal pain for 1 week, pelvic mass admission. Patients due to primary amenorrhea (23 years old) in the hospital by the pelvic pneumoperitoneum diagnosis of uterine ovarian hypoplasia. Chromosome examination was 45, × / 46, ××. Diagnosis of Turner’s syndrome, had